Name | PHENYLALANINE |
Synonyms | PHENYLALANINE Alanine, phenyl ester phenyl 2-aminopropanoate Alanine, phenyl ester (9CI) |
CAS | 167088-01-9 |
Molecular Formula | C9H11NO2 |
Molar Mass | 165.19 |
Density | 1.118±0.06 g/cm3(Predicted) |
Boling Point | 262.6±23.0 °C(Predicted) |
pKa | 7.44±0.29(Predicted) |
amino acid | phenylalanine is a kind of amino acid and sweet flavor intermediate, often used as medical raw materials, without any harm to human body, used as nutritional supplements, food additives, nutritional supplements, beverage additives. Phenylalanine is mainly a raw material for biosynthesis of anthocyanin and other flavonoids, and anthocyanin is mainly used for fruit color change, fruit color change is the process of accumulated temperature, light and sugar synthesis, the sugar content of the fruit increased and the acid content decreased during the color change period. At the same time, the substance of the mouth and the aromatic substances began to increase, and the soluble substances began to accumulate. |
genetic disease associated with phenylalanine | phenylalanine is one of the essential amino acids. Normal daily intake of about 200 to 500 mg, of which 1/3 for protein synthesis, and 2/3 through the conversion of phenylalanine hydroxylase (PAH) in liver cells into tyrosine, to synthesize adrenaline and melanin, etc. In addition to PAH, tetrahydrobiopterin (BH4) must be involved as a coenzyme in the conversion of phenylalanine to tyrosine. Gene mutation may cause the activity defect of related enzymes, resulting in abnormal accumulation of phenylalanine and its keto acid, and a large number of excretion from urine. The main clinical features were mental retardation, psychoneurotic symptoms, eczema, skin scratch sign, depigmentation and rat odor, and abnormal EEG. The disease is autosomal recessive inheritance. Schematic diagram of alanine-related diseases |